Involvement of temporal artery as a rare presentation of IgG4-related disease

Abstract

Immunoglobulin G4-related disease (IgG4-RD) is a chronic systemic condition characterized by fibroinflammatory features that can affect multiple organs. Ophthalmic involvement commonly presents with tumor-like masses, particularly in the lacrimal glands and orbital tissues. However, involvement of temporal artery as a rare manifestation of IgG4-RD has been infrequently reported in the literature. Herein, we present a case demonstrating neuro-ophthalmic involvement in which involvement of temporal artery emerged as a clinical manifestation of IgG4-related disease.